Congenital Afibrinogenemia presenting as antenatal intracranial bleed: a case report

نویسندگان

  • Gopakumar Hariharan
  • Sivji Ramachandran
  • Rajiv Parapurath
چکیده

Congenital afibrinogenemia is a very rare inherited coagulation disorder, characterized by virtual absence of plasma fibrinogen (factor I). There are only about 250 cases reported in the world literature 1. We describe a case of congenital afibrinogenemia which presented as an antenatally detected intracranial bleed.

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عنوان ژورنال:

دوره 36  شماره 

صفحات  -

تاریخ انتشار 2010